| Source | Code | Name | Case count | Share of cases (%) |
|---|---|---|---|---|
| OUTPAT | OUTPAT_ICD10(D8418) | Other specified defect in the complement system | 67 | |
| OUTPAT | OUTPAT_ICD10(D841) | Defects in the complement system | 49 | |
| OUTPAT | OUTPAT_ICD10(D8419) | Unspecified defect in the complement system | 45 | |
| OUTPAT | OUTPAT_ICD10(D8411) | Hereditary angioedema type I | 24 | |
| OUTPAT | OUTPAT_ICD10(D8413) | Hereditary angioedema type III | 15 | |
| INPAT | INPAT_ICD10(D8418) | Other specified defect in the complement system | 12 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(D8418) | Other specified defect in the complement system. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 11 | |
| INPAT | INPAT_ICD10(D841) | Defects in the complement system | 10 | |
| OUTPAT | OUTPAT_ICD10(D8412) | Hereditary angioedema type II | 9 | |
| INPAT | INPAT_ICD10(D8411) | Hereditary angioedema type I | 8 | |
| INPAT | INPAT_ICD10(D8419) | Unspecified defect in the complement system | 7 | |
| INPAT | INPAT_ICD10(D8413) | Hereditary angioedema type III | 6 | |
| OUTPAT | OUTPAT_ICD10(D8414) | C1 esterase inhibitor deficiency (C1-INH deficiency) | 5 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(D841) | Defects in the complement system. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 5 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(D8411) | Hereditary angioedema type I. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 5 |