Source Code Name Case count Share of cases (%)
OUTPAT OUTPAT_ICD10(D801) Nonfamilial hypogammaglobulinaemia 246
OUTPAT OUTPAT_ICD10(D809) Immunodeficiency with predominantly antibody defects, unspecified 187
OUTPAT OUTPAT_ICD10(D803) Selective deficiency of immunoglobulin G [IgG] subclasses 166
OUTPAT OUTPAT_ICD10(D808) Other immunodeficiencies with predominantly antibody defects 140
INPAT INPAT_ICD10(D801) Nonfamilial hypogammaglobulinaemia 125
OUTPAT OUTPAT_ICD10(D800) Hereditary hypogammaglobulinaemia 81
OUTPAT OUTPAT_ICD10(D802) Selective deficiency of immunoglobulin A [IgA] 79
OUTPAT OUTPAT_ICD10(D814) Nezelof's syndrome 69
OUTPAT OUTPAT_ICD10(D8418) Other specified defect in the complement system 67
REIMB REIMB_KELA(120)_ICD10(D80) Hypogammaglobulinaemia, Immunodeficiency with predominantly antibody defects 63
OUTPAT OUTPAT_ICD10(D849) Immunodeficiency, unspecified 60
INPAT INPAT_ICD10(D810) Severe combined immunodeficiency [SCID] with reticular dysgenesis 59
INPAT INPAT_ICD10(D809) Immunodeficiency with predominantly antibody defects, unspecified 58
OUTPAT OUTPAT_ICD10(D830) Common variable immunodeficiency with predominant abnormalities of B-cell numbers and function 57
OUTPAT OUTPAT_ICD10(D839) Common variable immunodeficiency, unspecified 57
INPAT INPAT_ICD10(D814) Nezelof's syndrome 56
OUTPAT OUTPAT_ICD10(D841) Defects in the complement system 49
INPAT INPAT_ICD10(D803) Selective deficiency of immunoglobulin G [IgG] subclasses 48
OUTPAT OUTPAT_ICD10(D8419) Unspecified defect in the complement system 45
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(D801) Nonfamilial hypogammaglobulinaemia. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 43
REIMB REIMB_KELA(120)_ICD10(D801) Hypogammaglobulinaemia, Nonfamilial hypogammaglobulinaemia 40
INPAT INPAT_ICD10(D808) Other immunodeficiencies with predominantly antibody defects 35
OUTPAT OUTPAT_ICD10(D806) Antibody deficiency with near-normal immunoglobulins or with hyperimmunoglobulinaemia 32
INPAT INPAT_ICD10(D839) Common variable immunodeficiency, unspecified 30
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(D803) Selective deficiency of immunoglobulin G [IgG] subclasses. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 30
OUTPAT OUTPAT_ICD10(D810) Severe combined immunodeficiency [SCID] with reticular dysgenesis 29
OUTPAT OUTPAT_ICD10(D838) Other common variable immunodeficiencies 27
INPAT INPAT_ICD10(D802) Selective deficiency of immunoglobulin A [IgA] 25
OUTPAT OUTPAT_ICD10(D8411) Hereditary angioedema type I 24
OUTPAT OUTPAT_ICD10(D848) Other specified immunodeficiencies 23
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(D808) Other immunodeficiencies with predominantly antibody defects. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 23
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(D809) Immunodeficiency with predominantly antibody defects, unspecified. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 23
OUTPAT OUTPAT_ICD10(D831) Common variable immunodeficiency with predominant immunoregulatory T-cell disorders 22
OUTPAT OUTPAT_ICD10(D818) Other combined immunodeficiencies 21
INPAT INPAT_ICD10(D800) Hereditary hypogammaglobulinaemia 20
OUTPAT OUTPAT_ICD10(D819) Combined immunodeficiency, unspecified 19
INPAT INPAT_ICD9(2790B) Disorders involving the immune mechanism, Deficiency of humoral immunity 18
INPAT INPAT_ICD10(D806) Antibody deficiency with near-normal immunoglobulins or with hyperimmunoglobulinaemia 17
INPAT INPAT_ICD10(D849) Immunodeficiency, unspecified 17
INPAT INPAT_ICD9(2790C) Disorders involving the immune mechanism, Deficiency of humoral immunity 17
INPAT INPAT_ICD10(D818) Other combined immunodeficiencies 16
OUTPAT OUTPAT_ICD10(D811) Severe combined immunodeficiency [SCID] with low T- and B-cell numbers 16
REIMB REIMB_KELA(120)_ICD10(D808) Hypogammaglobulinaemia, Other immunodeficiencies with predominantly antibody defects 16
INPAT INPAT_ICD10(D840) Lymphocyte function antigen-1 [LFA-1] defect 15
OUTPAT OUTPAT_ICD10(D8413) Hereditary angioedema type III 15
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(D802) Selective deficiency of immunoglobulin A [IgA]. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 15
REIMB REIMB_KELA(120)_ICD10(D809) Hypogammaglobulinaemia, Immunodeficiency with predominantly antibody defects, unspecified 15
REIMB REIMB_KELA(120)_ICD8(NA) Hypogammaglobulinaemia, Name not found 15
INPAT INPAT_ICD10(D830) Common variable immunodeficiency with predominant abnormalities of B-cell numbers and function 14
INPAT INPAT_ICD10(D838) Other common variable immunodeficiencies 14
OUTPAT OUTPAT_ICD10(D824) Hyperimmunoglobulin E [IgE] syndrome 14
INPAT INPAT_ICD10(D831) Common variable immunodeficiency with predominant immunoregulatory T-cell disorders 12
INPAT INPAT_ICD10(D8418) Other specified defect in the complement system 12
OUTPAT OUTPAT_ICD10(D840) Lymphocyte function antigen-1 [LFA-1] defect 12
OUTPAT OUTPAT_ICD10(D804) Selective deficiency of immunoglobulin M [IgM] 11
OUTPAT OUTPAT_ICD10(D821) Di George's syndrome 11
OUTPAT OUTPAT_ICD10(D822) Immunodeficiency with short-limbed stature 11
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(D800) Hereditary hypogammaglobulinaemia. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 11
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(D8418) Other specified defect in the complement system. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 11
REIMB REIMB_KELA(120)_ICD10(D803) Hypogammaglobulinaemia, Selective deficiency of immunoglobulin G [IgG] subclasses 11
REIMB REIMB_KELA(120)_ICD10(D83) Hypogammaglobulinaemia, Common variable immunodeficiency 11
INPAT INPAT_ICD10(D812) Severe combined immunodeficiency [SCID] with low or normal B-cell numbers 10
INPAT INPAT_ICD10(D841) Defects in the complement system 10
REIMB REIMB_KELA(120)_ICD10(D839) Hypogammaglobulinaemia, Common variable immunodeficiency, unspecified 10
INPAT INPAT_ICD9(2790A) Disorders involving the immune mechanism, Deficiency of humoral immunity 9
OUTPAT OUTPAT_ICD10(D8412) Hereditary angioedema type II 9
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(D82) Immunodeficiency associated with other major defects. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 9
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(D839) Common variable immunodeficiency, unspecified. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 9
DEATH DEATH_ICD10(D801) Nonfamilial hypogammaglobulinaemia 8
INPAT INPAT_ICD10(D819) Combined immunodeficiency, unspecified 8
INPAT INPAT_ICD10(D824) Hyperimmunoglobulin E [IgE] syndrome 8
INPAT INPAT_ICD10(D8411) Hereditary angioedema type I 8
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(D849) Immunodeficiency, unspecified. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 8
INPAT INPAT_ICD10(D822) Immunodeficiency with short-limbed stature 7
INPAT INPAT_ICD10(D828) Immunodeficiency associated with other specified major defects 7
INPAT INPAT_ICD10(D8419) Unspecified defect in the complement system 7
INPAT INPAT_ICD10(D848) Other specified immunodeficiencies 7
OUTPAT OUTPAT_ICD10(D805) Immunodeficiency with increased immunoglobulin M [IgM] 7
OUTPAT OUTPAT_ICD10(D828) Immunodeficiency associated with other specified major defects 7
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(D848) Other specified immunodeficiencies. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 7
REIMB REIMB_KELA(120)_ICD10(D830) Hypogammaglobulinaemia, Common variable immunodeficiency with predominant abnormalities of B-cell numbers and function 7
REIMB REIMB_KELA(120)_ICD9(NA) Hypogammaglobulinaemia, Name not found 7
INPAT INPAT_ICD10(D811) Severe combined immunodeficiency [SCID] with low T- and B-cell numbers 6
INPAT INPAT_ICD10(D813) Adenosine deaminase [ADA] deficiency 6
INPAT INPAT_ICD10(D8413) Hereditary angioedema type III 6
OUTPAT OUTPAT_ICD10(D812) Severe combined immunodeficiency [SCID] with low or normal B-cell numbers 6
INPAT INPAT_ICD10(D821) Di George's syndrome 5
OUTPAT OUTPAT_ICD10(D829) Immunodeficiency associated with major defect, unspecified 5
OUTPAT OUTPAT_ICD10(D8414) C1 esterase inhibitor deficiency (C1-INH deficiency) 5
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(D824) Hyperimmunoglobulin E [IgE] syndrome. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 5
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(D84) Other immunodeficiencies. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 5
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(D841) Defects in the complement system. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 5
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(D8411) Hereditary angioedema type I. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 5