Source Code Name Case count Share of cases (%)
OUTPAT OUTPAT_ICD10(D8418) Other specified defect in the complement system 67
OUTPAT OUTPAT_ICD10(D849) Immunodeficiency, unspecified 60
OUTPAT OUTPAT_ICD10(D841) Defects in the complement system 49
OUTPAT OUTPAT_ICD10(D8419) Unspecified defect in the complement system 45
OUTPAT OUTPAT_ICD10(D8411) Hereditary angioedema type I 24
OUTPAT OUTPAT_ICD10(D848) Other specified immunodeficiencies 23
INPAT INPAT_ICD10(D849) Immunodeficiency, unspecified 17
INPAT INPAT_ICD10(D840) Lymphocyte function antigen-1 [LFA-1] defect 15
OUTPAT OUTPAT_ICD10(D8413) Hereditary angioedema type III 15
INPAT INPAT_ICD10(D8418) Other specified defect in the complement system 12
OUTPAT OUTPAT_ICD10(D840) Lymphocyte function antigen-1 [LFA-1] defect 12
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(D8418) Other specified defect in the complement system. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 11
INPAT INPAT_ICD10(D841) Defects in the complement system 10
OUTPAT OUTPAT_ICD10(D8412) Hereditary angioedema type II 9
INPAT INPAT_ICD10(D8411) Hereditary angioedema type I 8
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(D849) Immunodeficiency, unspecified. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 8
INPAT INPAT_ICD10(D8419) Unspecified defect in the complement system 7
INPAT INPAT_ICD10(D848) Other specified immunodeficiencies 7
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(D848) Other specified immunodeficiencies. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 7
INPAT INPAT_ICD10(D8413) Hereditary angioedema type III 6
OUTPAT OUTPAT_ICD10(D8414) C1 esterase inhibitor deficiency (C1-INH deficiency) 5
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(D84) Other immunodeficiencies. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 5
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(D841) Defects in the complement system. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 5
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(D8411) Hereditary angioedema type I. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 5