Source Code Name Case count Share of cases (%)
OUTPAT OUTPAT_ICD10(G122) Motor neuron disease 377
INPAT INPAT_ICD10(G122) Motor neuron disease 293
DEATH DEATH_ICD10(G122) Motor neuron disease 171
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(G122) Motor neuron disease. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 142
OUTPAT OUTPAT_ICD10(G119) Hereditary ataxia, unspecified 133
OUTPAT OUTPAT_ICD10(G129) Spinal muscular atrophy, unspecified 81
OUTPAT OUTPAT_ICD10(G112) Late-onset cerebellar ataxia 64
INPAT INPAT_ICD10(G119) Hereditary ataxia, unspecified 57
INPAT INPAT_ICD9(1380A) Late effects of acute poliomyelitis 57
OUTPAT OUTPAT_ICD10(G128) Other spinal muscular atrophies and related syndromes 51
OUTPAT OUTPAT_ICD10(G118) Other hereditary ataxias 41
OUTPAT OUTPAT_ICD10(G121) Other inherited spinal muscular atrophy 36
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(G119) Hereditary ataxia, unspecified. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 31
INPAT INPAT_ICD10(G129) Spinal muscular atrophy, unspecified 29
OUTPAT OUTPAT_ICD10(G10) Huntington's disease 27
OUTPAT OUTPAT_ICD10(G114) Hereditary spastic paraplegia 25
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(G112) Late-onset cerebellar ataxia. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 23
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(G129) Spinal muscular atrophy, unspecified. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 23
INPAT INPAT_ICD10(G112) Late-onset cerebellar ataxia 21
INPAT INPAT_ICD10(G121) Other inherited spinal muscular atrophy 20
INPAT INPAT_ICD8(34899) Motor neurone disease, Other and unspecified manifestations 17
INPAT INPAT_ICD9(3342A) Primary cerebellar degeneration 17
INPAT INPAT_ICD10(G118) Other hereditary ataxias 16
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(G128) Other spinal muscular atrophies and related syndromes. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 16
INPAT INPAT_ICD10(G128) Other spinal muscular atrophies and related syndromes 15
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(G121) Other inherited spinal muscular atrophy. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 15
INPAT INPAT_ICD10(G10) Huntington's disease 12
OUTPAT OUTPAT_ICD10(G130) Paraneoplastic neuromyopathy and neuropathy 12
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(G114) Hereditary spastic paraplegia. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 11
INPAT INPAT_ICD10(G114) Hereditary spastic paraplegia 10
INPAT INPAT_ICD9(3343A) Other cerebellar ataxia 10
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(G1102) Dysequilibrium syndrome. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 10
DEATH DEATH_ICD9(3352A) Anterior horn cell disease, Motor neuron disease 9
INPAT INPAT_ICD10(G130) Paraneoplastic neuromyopathy and neuropathy 9
OUTPAT OUTPAT_ICD10(G1100) Cerebellar dysplasia and aplasia 9
INPAT INPAT_ICD9(3349X) Spinocerebellar disease, unspecified 8
INPAT INPAT_ICD9(3351X) Anterior horn cell disease, Spinal muscular atrophy 8
OUTPAT OUTPAT_ICD10(G1118) Early-onset cerebellar ataxia 8
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(G11) Hereditary ataxia. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 8
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(G118) Other hereditary ataxias. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 8
INPAT INPAT_ICD8(34800) Motor neurone disease, Amyotrophic lateral sclerosis 7
INPAT INPAT_ICD8(34898) Motor neurone disease, Alii definiti 7
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(G10) Huntington's disease. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 6
INPAT INPAT_ICD10(G120) Infantile spinal muscular atrophy, type I [Werdnig-Hoffman] 5
OUTPAT OUTPAT_ICD10(G120) Infantile spinal muscular atrophy, type I [Werdnig-Hoffman] 5