Source Code Name Case count Share of cases (%)
OUTPAT OUTPAT_ICD10(M315) Giant cell arteritis with polymyalgia rheumatica 757
INPAT INPAT_ICD10(M315) Giant cell arteritis with polymyalgia rheumatica 449
OUTPAT OUTPAT_ICD10(M313) Wegener's granulomatosis 386
INPAT INPAT_ICD10(M313) Wegener's granulomatosis 271
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M315) Giant cell arteritis with polymyalgia rheumatica. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 239
OUTPAT OUTPAT_ICD10(M319) Necrotizing vasculopathy, unspecified 162
OUTPAT OUTPAT_ICD10(M316) Other giant cell arteritis 153
OUTPAT OUTPAT_ICD10(M317) Microscopic polyangiitis 126
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M313) Wegener's granulomatosis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 116
OUTPAT OUTPAT_ICD10(M311) Thrombotic microangiopathy 111
INPAT INPAT_ICD10(M319) Necrotizing vasculopathy, unspecified 101
OUTPAT OUTPAT_ICD10(M310) Hypersensitivity angiitis 92
OUTPAT OUTPAT_ICD10(M318) Other specified necrotizing vasculopathies 87
INPAT INPAT_ICD10(M316) Other giant cell arteritis 79
INPAT INPAT_ICD10(M311) Thrombotic microangiopathy 77
INPAT INPAT_ICD10(M317) Microscopic polyangiitis 69
INPAT INPAT_ICD10(M310) Hypersensitivity angiitis 55
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M316) Other giant cell arteritis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 50
INPAT INPAT_ICD10(M318) Other specified necrotizing vasculopathies 48
INPAT INPAT_ICD9(4476A) Arteritis, unspecified 43
OUTPAT OUTPAT_ICD10(M314) Aortic arch syndrome [Takayasu] 40
INPAT INPAT_ICD10(M314) Aortic arch syndrome [Takayasu] 28
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M317) Microscopic polyangiitis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 24
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M319) Necrotizing vasculopathy, unspecified. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 24
INPAT INPAT_ICD8(44698) Polyarteritis nodosa and allied conditions, Other 23
DEATH DEATH_ICD10(M313) Wegener's granulomatosis 22
INPAT INPAT_ICD9(4462A) Hypersensitivity angiitis 21
INPAT INPAT_ICD9(4465A) Giant cell arteritis 18
INPAT INPAT_ICD9(4464A) Wegener's granulomatosis 16
OUTPAT OUTPAT_ICD10(M312) Lethal midline granuloma 13
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M314) Aortic arch syndrome [Takayasu]. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 13
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M310) Hypersensitivity angiitis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 12
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M318) Other specified necrotizing vasculopathies. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 9
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M311) Thrombotic microangiopathy. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 8
DEATH DEATH_ICD10(M317) Microscopic polyangiitis 5
INPAT INPAT_ICD10(M312) Lethal midline granuloma 5
INPAT INPAT_ICD9(4466A) Thrombotic microangiopathy 5
INPAT INPAT_ICD9(4467A) Takayasu's disease 5