| Source | Code | Name | Case count | Share of cases (%) |
|---|---|---|---|---|
| OUTPAT | OUTPAT_ICD10(M315) | Giant cell arteritis with polymyalgia rheumatica | 757 | |
| INPAT | INPAT_ICD10(M315) | Giant cell arteritis with polymyalgia rheumatica | 449 | |
| OUTPAT | OUTPAT_ICD10(M313) | Wegener's granulomatosis | 386 | |
| INPAT | INPAT_ICD10(M313) | Wegener's granulomatosis | 271 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M315) | Giant cell arteritis with polymyalgia rheumatica. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 239 | |
| OUTPAT | OUTPAT_ICD10(M319) | Necrotizing vasculopathy, unspecified | 162 | |
| OUTPAT | OUTPAT_ICD10(M316) | Other giant cell arteritis | 153 | |
| OUTPAT | OUTPAT_ICD10(M317) | Microscopic polyangiitis | 126 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M313) | Wegener's granulomatosis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 116 | |
| OUTPAT | OUTPAT_ICD10(M311) | Thrombotic microangiopathy | 111 | |
| INPAT | INPAT_ICD10(M319) | Necrotizing vasculopathy, unspecified | 101 | |
| OUTPAT | OUTPAT_ICD10(M310) | Hypersensitivity angiitis | 92 | |
| OUTPAT | OUTPAT_ICD10(M318) | Other specified necrotizing vasculopathies | 87 | |
| INPAT | INPAT_ICD10(M316) | Other giant cell arteritis | 79 | |
| INPAT | INPAT_ICD10(M311) | Thrombotic microangiopathy | 77 | |
| INPAT | INPAT_ICD10(M317) | Microscopic polyangiitis | 69 | |
| INPAT | INPAT_ICD10(M310) | Hypersensitivity angiitis | 55 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M316) | Other giant cell arteritis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 50 | |
| INPAT | INPAT_ICD10(M318) | Other specified necrotizing vasculopathies | 48 | |
| INPAT | INPAT_ICD9(4476A) | Arteritis, unspecified | 43 | |
| OUTPAT | OUTPAT_ICD10(M314) | Aortic arch syndrome [Takayasu] | 40 | |
| INPAT | INPAT_ICD10(M314) | Aortic arch syndrome [Takayasu] | 28 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M317) | Microscopic polyangiitis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 24 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M319) | Necrotizing vasculopathy, unspecified. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 24 | |
| INPAT | INPAT_ICD8(44698) | Polyarteritis nodosa and allied conditions, Other | 23 | |
| DEATH | DEATH_ICD10(M313) | Wegener's granulomatosis | 22 | |
| INPAT | INPAT_ICD9(4462A) | Hypersensitivity angiitis | 21 | |
| INPAT | INPAT_ICD9(4465A) | Giant cell arteritis | 18 | |
| INPAT | INPAT_ICD9(4464A) | Wegener's granulomatosis | 16 | |
| OUTPAT | OUTPAT_ICD10(M312) | Lethal midline granuloma | 13 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M314) | Aortic arch syndrome [Takayasu]. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 13 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M310) | Hypersensitivity angiitis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 12 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M318) | Other specified necrotizing vasculopathies. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 9 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M311) | Thrombotic microangiopathy. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 8 | |
| DEATH | DEATH_ICD10(M317) | Microscopic polyangiitis | 5 | |
| INPAT | INPAT_ICD10(M312) | Lethal midline granuloma | 5 | |
| INPAT | INPAT_ICD9(4466A) | Thrombotic microangiopathy | 5 | |
| INPAT | INPAT_ICD9(4467A) | Takayasu's disease | 5 |