Source Code Name Case count Share of cases (%)
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M353) Polymyalgia rheumatica. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 2727
OUTPAT OUTPAT_ICD10(M353) Polymyalgia rheumatica 2594
OUTPAT OUTPAT_ICD10(M350) Sicca syndrome [Sjögren] 2120
INPAT INPAT_ICD10(M353) Polymyalgia rheumatica 1431
OUTPAT OUTPAT_ICD10(M359) Systemic involvement of connective tissue, unspecified 1201
OUTPAT OUTPAT_ICD10(M357) Hypermobility syndrome 1175
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M350) Sicca syndrome [Sjögren]. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 936
OUTPAT OUTPAT_ICD10(M315) Giant cell arteritis with polymyalgia rheumatica 757
OUTPAT OUTPAT_ICD10(M329) Systemic lupus erythematosus, unspecified 728
INPAT INPAT_ICD10(M350) Sicca syndrome [Sjögren] 721
INPAT INPAT_ICD10(M315) Giant cell arteritis with polymyalgia rheumatica 449
OUTPAT OUTPAT_ICD10(M351) Other overlap syndromes 434
OUTPAT OUTPAT_ICD10(M313) Wegener's granulomatosis 386
INPAT INPAT_ICD10(M329) Systemic lupus erythematosus, unspecified 371
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M357) Hypermobility syndrome. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 354
INPAT INPAT_ICD10(M359) Systemic involvement of connective tissue, unspecified 324
OUTPAT OUTPAT_ICD10(M341) CR(E)ST syndrome 324
INPAT INPAT_ICD10(M313) Wegener's granulomatosis 271
INPAT INPAT_ICD10(M357) Hypermobility syndrome 269
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M329) Systemic lupus erythematosus, unspecified. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 250
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M315) Giant cell arteritis with polymyalgia rheumatica. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 239
OUTPAT OUTPAT_ICD10(M349) Systemic sclerosis, unspecified 229
OUTPAT OUTPAT_ICD10(M321) Systemic lupus erythematosus with organ or system involvement 209
OUTPAT OUTPAT_ICD10(M328) Other forms of systemic lupus erythematosus 200
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M359) Systemic involvement of connective tissue, unspecified. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 192
OUTPAT OUTPAT_ICD10(M332) Polymyositis 179
OUTPAT OUTPAT_ICD10(M319) Necrotizing vasculopathy, unspecified 162
INPAT INPAT_ICD10(M351) Other overlap syndromes 153
OUTPAT OUTPAT_ICD10(M316) Other giant cell arteritis 153
INPAT INPAT_ICD9(7100A) Systemic lupus erythematosus 151
OUTPAT OUTPAT_ICD10(M320) Drug-induced systemic lupus erythematosus 149
INPAT INPAT_ICD10(M321) Systemic lupus erythematosus with organ or system involvement 142
OUTPAT OUTPAT_ICD10(M358) Other specified systemic involvement of connective tissue 129
OUTPAT OUTPAT_ICD10(M317) Microscopic polyangiitis 126
OUTPAT OUTPAT_ICD10(M355) Multifocal fibrosclerosis 123
OUTPAT OUTPAT_ICD10(M339) Dermatopolymyositis, unspecified 120
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M341) CR(E)ST syndrome. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 118
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M313) Wegener's granulomatosis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 116
OUTPAT OUTPAT_ICD10(M311) Thrombotic microangiopathy 111
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M351) Other overlap syndromes. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 111
OUTPAT OUTPAT_ICD10(M300) Polyarteritis nodosa 109
OUTPAT OUTPAT_ICD10(M331) Other dermatomyositis 108
INPAT INPAT_ICD10(M332) Polymyositis 105
INPAT INPAT_ICD10(M341) CR(E)ST syndrome 105
INPAT INPAT_ICD10(M319) Necrotizing vasculopathy, unspecified 101
OUTPAT OUTPAT_ICD10(M340) Progressive systemic sclerosis 99
OUTPAT OUTPAT_ICD10(M310) Hypersensitivity angiitis 92
OUTPAT OUTPAT_ICD10(M318) Other specified necrotizing vasculopathies 87
INPAT INPAT_ICD9(7250A) Polymyalgia rheumatica 85
OUTPAT OUTPAT_ICD10(M301) Polyarteritis with lung involvement [Churg-Strauss] 85
INPAT INPAT_ICD10(M316) Other giant cell arteritis 79
INPAT INPAT_ICD10(M300) Polyarteritis nodosa 78
INPAT INPAT_ICD10(M328) Other forms of systemic lupus erythematosus 78
INPAT INPAT_ICD10(M311) Thrombotic microangiopathy 77
INPAT INPAT_ICD10(M349) Systemic sclerosis, unspecified 77
INPAT INPAT_ICD8(73491) Diffuse diseases of connective tissue, Collagenosis NUD 72
INPAT INPAT_ICD10(M317) Microscopic polyangiitis 69
OUTPAT OUTPAT_ICD10(M352) Behçet's disease 69
INPAT INPAT_ICD9(7102B) Diffuse diseases of connective tissue, Sicca syndrome 68
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M32) Systemic lupus erythematosus. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 68
INPAT INPAT_ICD10(M339) Dermatopolymyositis, unspecified 67
INPAT INPAT_ICD9(7109X) Unspecified diffuse connective tissue disease 62
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M349) Systemic sclerosis, unspecified. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 59
OUTPAT OUTPAT_ICD10(M348) Other forms of systemic sclerosis 58
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M332) Polymyositis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 57
INPAT INPAT_ICD10(M310) Hypersensitivity angiitis 55
INPAT INPAT_ICD10(M320) Drug-induced systemic lupus erythematosus 55
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M328) Other forms of systemic lupus erythematosus. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 52
OUTPAT OUTPAT_ICD10(M308) Other conditions related to polyarteritis nodosa 51
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M316) Other giant cell arteritis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 50
INPAT INPAT_ICD9(7102A) Diffuse diseases of connective tissue, Sicca syndrome 49
INPAT INPAT_ICD10(M301) Polyarteritis with lung involvement [Churg-Strauss] 48
INPAT INPAT_ICD10(M318) Other specified necrotizing vasculopathies 48
INPAT INPAT_ICD10(M331) Other dermatomyositis 47
INPAT INPAT_ICD10(M355) Multifocal fibrosclerosis 47
INPAT INPAT_ICD9(4476A) Arteritis, unspecified 43
INPAT INPAT_ICD10(M308) Other conditions related to polyarteritis nodosa 40
INPAT INPAT_ICD10(M340) Progressive systemic sclerosis 40
OUTPAT OUTPAT_ICD10(M314) Aortic arch syndrome [Takayasu] 40
OUTPAT OUTPAT_ICD10(M32) Systemic lupus erythematosus 40
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M35) Other systemic involvement of connective tissue. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 39
OUTPAT OUTPAT_ICD10(M354) Diffuse (eosinophilic) fasciitis 36
INPAT INPAT_ICD10(M358) Other specified systemic involvement of connective tissue 34
INPAT INPAT_ICD10(M303) Mucocutaneous lymph node syndrome [Kawasaki] 32
INPAT INPAT_ICD10(M348) Other forms of systemic sclerosis 30
OUTPAT OUTPAT_ICD10(M303) Mucocutaneous lymph node syndrome [Kawasaki] 30
INPAT INPAT_ICD10(M352) Behçet's disease 29
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M358) Other specified systemic involvement of connective tissue. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 29
INPAT INPAT_ICD10(M314) Aortic arch syndrome [Takayasu] 28
OUTPAT OUTPAT_ICD10(M330) Juvenile dermatomyositis 28
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M321) Systemic lupus erythematosus with organ or system involvement. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 28
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M339) Dermatopolymyositis, unspecified. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 28
INPAT INPAT_ICD9(7108X) Other specified diffuse diseases of connective tissue 25
INPAT INPAT_ICD8(73490) Diffuse diseases of connective tissue, Keratoconjunctivitis sicca (dry eye disease). Sjögren's syndrome 24
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M317) Microscopic polyangiitis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 24
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M319) Necrotizing vasculopathy, unspecified. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 24
INPAT INPAT_ICD8(44698) Polyarteritis nodosa and allied conditions, Other 23
OUTPAT OUTPAT_ICD10(M364) Arthropathy in hypersensitivity reactions classified elsewhere 23
OUTPAT OUTPAT_ICD10(M368) Systemic disorders of connective tissue in other diseases classified elsewhere 23
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M301) Polyarteritis with lung involvement [Churg-Strauss]. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 23
DEATH DEATH_ICD10(M313) Wegener's granulomatosis 22
INPAT INPAT_ICD9(4462A) Hypersensitivity angiitis 21
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M300) Polyarteritis nodosa. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 21
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M331) Other dermatomyositis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 21
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M34) Systemic sclerosis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 21
OUTPAT OUTPAT_ICD10(M35) Other systemic involvement of connective tissue 20
DEATH DEATH_ICD10(M353) Polymyalgia rheumatica 19
INPAT INPAT_ICD8(73498) Diffuse diseases of connective tissue, Alii definiti 19
INPAT INPAT_ICD9(7101A) Diffuse diseases of connective tissue, Systemic sclerosis 19
INPAT INPAT_ICD10(M354) Diffuse (eosinophilic) fasciitis 18
INPAT INPAT_ICD9(4465A) Giant cell arteritis 18
OUTPAT OUTPAT_ICD10(M362) Haemophilic arthropathy (D66-D68+) 18
INPAT INPAT_ICD10(M330) Juvenile dermatomyositis 17
INPAT INPAT_ICD8(71610) Polymyositis and dermatomyositis, Polymyositis 17
INPAT INPAT_ICD9(4464A) Wegener's granulomatosis 16
INPAT INPAT_ICD8(44638) Polyarteritis nodosa and allied conditions, Polymyalgia arteritica (rheumatica) 15
INPAT INPAT_ICD9(4461A) Acute febrile mucocutaneous lymph node syndrome [MCLS] 15
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M348) Other forms of systemic sclerosis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 15
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M352) Behçet's disease. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 15
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M340) Progressive systemic sclerosis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 14
INPAT INPAT_ICD8(71600) Polymyositis and dermatomyositis, Dermatomyositis 13
INPAT INPAT_ICD9(7104A) Polymyositis 13
OUTPAT OUTPAT_ICD10(M312) Lethal midline granuloma 13
OUTPAT OUTPAT_ICD10(M361) Arthropathy in neoplastic disease (C00-D48+) 13
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M314) Aortic arch syndrome [Takayasu]. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 13
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M354) Diffuse (eosinophilic) fasciitis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 13
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M355) Multifocal fibrosclerosis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 13
INPAT INPAT_ICD8(73499) Diffuse diseases of connective tissue, Other and unspecified 12
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M310) Hypersensitivity angiitis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 12
INPAT INPAT_ICD9(7103B) Diffuse diseases of connective tissue, Dermatomyositis 11
DEATH DEATH_ICD10(M332) Polymyositis 10
DEATH DEATH_ICD10(M350) Sicca syndrome [Sjögren] 10
INPAT INPAT_ICD10(M362) Haemophilic arthropathy (D66-D68+) 10
INPAT INPAT_ICD10(M368) Systemic disorders of connective tissue in other diseases classified elsewhere 10
INPAT INPAT_ICD9(4460A) Polyarteritis nodosa and allied conditions, Polyarteritis nodosa 10
INPAT INPAT_ICD8(44630) Polyarteritis nodosa and allied conditions, Arteritis cranialis (temporalis) 9
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M30) Polyarteritis nodosa and related conditions. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 9
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M318) Other specified necrotizing vasculopathies. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 9
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M364) Arthropathy in hypersensitivity reactions classified elsewhere. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 9
DEATH DEATH_ICD10(M329) Systemic lupus erythematosus, unspecified 8
INPAT INPAT_ICD10(M361) Arthropathy in neoplastic disease (C00-D48+) 8
INPAT INPAT_ICD10(M364) Arthropathy in hypersensitivity reactions classified elsewhere 8
INPAT INPAT_ICD8(44600) Polyarteritis nodosa and allied conditions, Polyarteritis nodosa 8
INPAT INPAT_ICD8(73409) Diffuse diseases of connective tissue, Sclerosis systematica NUD 8
INPAT INPAT_ICD9(7103A) Diffuse diseases of connective tissue, Dermatomyositis 8
OUTPAT OUTPAT_ICD10(M356) Relapsing panniculitis [Weber-Christian] 8
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M311) Thrombotic microangiopathy. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 8
DEATH DEATH_ICD10(M341) CR(E)ST syndrome 7
DEATH DEATH_ICD10(M359) Systemic involvement of connective tissue, unspecified 7
INPAT INPAT_ICD8(74310) Other congenital anomalies of nervous system, Microcephalus 7
OUTPAT OUTPAT_ICD10(M34) Systemic sclerosis 6
OUTPAT OUTPAT_ICD10(M342) Systemic sclerosis induced by drugs and chemicals 6
OUTPAT OUTPAT_ICD10(M360) Dermato(poly)myositis in neoplastic disease (C00-D48+) 6
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M308) Other conditions related to polyarteritis nodosa. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 6
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M33) Dermatopolymyositis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 6
DEATH DEATH_ICD10(M300) Polyarteritis nodosa 5
DEATH DEATH_ICD10(M317) Microscopic polyangiitis 5
DEATH DEATH_ICD10(M331) Other dermatomyositis 5
INPAT INPAT_ICD10(M312) Lethal midline granuloma 5
INPAT INPAT_ICD10(M356) Relapsing panniculitis [Weber-Christian] 5
INPAT INPAT_ICD8(73401) Diffuse diseases of connective tissue, Sclerosis systematica acrosclerotica 5
INPAT INPAT_ICD9(4466A) Thrombotic microangiopathy 5
INPAT INPAT_ICD9(4467A) Takayasu's disease 5
OUTPAT OUTPAT_ICD10(M302) Juvenile polyarteritis 5
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M362) Haemophilic arthropathy (D66-D68+). Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 5