| Source | Code | Name | Case count | Share of cases (%) |
|---|---|---|---|---|
| OUTPAT | OUTPAT_ICD10(Q8500) | Neurofibromatosis, type 1 | 162 | |
| OUTPAT | OUTPAT_ICD10(Q8509) | Unspecified neurofibromatosis | 93 | |
| INPAT | INPAT_ICD10(Q8500) | Neurofibromatosis, type 1 | 89 | |
| OUTPAT | OUTPAT_ICD10(Q851) | Tuberous sclerosis | 52 | |
| INPAT | INPAT_ICD10(Q8509) | Unspecified neurofibromatosis | 50 | |
| OUTPAT | OUTPAT_ICD10(Q8501) | Neurofibromatosis, type 2 | 43 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(Q8500) | Neurofibromatosis, type 1. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 40 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(Q850) | Neurofibromatosis (nonmalignant). Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 36 | |
| OUTPAT | OUTPAT_ICD10(Q850) | Neurofibromatosis (nonmalignant) | 31 | |
| INPAT | INPAT_ICD10(Q851) | Tuberous sclerosis | 25 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(Q8509) | Unspecified neurofibromatosis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 23 | |
| OUTPAT | OUTPAT_ICD10(Q859) | Phakomatosis, unspecified | 21 | |
| OUTPAT | OUTPAT_ICD10(Q8582) | of Hipple-Lindau syndrome | 20 | |
| INPAT | INPAT_ICD10(Q850) | Neurofibromatosis (nonmalignant) | 18 | |
| INPAT | INPAT_ICD10(Q8501) | Neurofibromatosis, type 2 | 17 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(Q851) | Tuberous sclerosis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 14 | |
| INPAT | INPAT_ICD10(Q8582) | of Hipple-Lindau syndrome | 13 | |
| OUTPAT | OUTPAT_ICD10(Q8580) | Peutz-Jegher syndrome | 10 | |
| INPAT | INPAT_ICD10(Q859) | Phakomatosis, unspecified | 9 | |
| OUTPAT | OUTPAT_ICD10(Q8588) | Other phakomatoses, not elsewhere classified | 9 | |
| OUTPAT | OUTPAT_ICD10(Q8581) | Sturge-Weber syndrome | 7 | |
| DEATH | DEATH_ICD10(Q850) | Neurofibromatosis (nonmalignant) | 6 | |
| OUTPAT | OUTPAT_ICD10(Q8583) | Gardner syndrome | 6 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(Q8582) | of Hipple-Lindau syndrome. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 6 | |
| INPAT | INPAT_ICD10(Q8581) | Sturge-Weber syndrome | 5 |